Stages of Rett Syndrome

  • Early Onset (between 6 – 18 months)

  • Rapid destructive phase – between 1 – 4 years

  • Plateau Stage – symptoms get no worse or their intensity lessens

  • Late motor deterioration – starts between 5 and 25 years of age and can last for decades

  • Pre-Regression Stage- <1 Year

  • Developmental Stagnation -
    9-24 months

  • Stage of Regression
    1-4 years

  • Early Post- Regression Stage-
    Preschool -early school years

  • Late Post- Regression stage -
    5-15-25 Years ++